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Atypical Rasmussen’s encephalitis presenting as focal status epilepticus and periodic generalised myoclonus

Atypical Rasmussen’s encephalitis presenting as focal status epilepticus and periodic generalised... Acta Neurologica Belgica https://doi.org/10.1007/s13760-023-02267-1 LE T TER TO  THE   EDITOR Atypical Rasmussen’s encephalitis presenting as focal status epilepticus and periodic generalised myoclonus 1 2 3 Pavan Kumar Rudrabhatla  · Fazala Mehnaz  · Srinivas Metta Received: 20 September 2022 / Accepted: 5 April 2023 © The Author(s) under exclusive licence to Belgian Neurological Society 2023 Introduction twitching. He was given loading dose of intravenous (IV) phenytoin (PHT) elsewhere, but seizures persisted with no Rasmussen’s encephalitis (RE) is a rare chronic neuro- improvement in sensorium between the events. In the emer- logical disorder, first described by Theodore Rasmussen, gency room he was given loading dose (25 mg/kg) of IV a neurosurgeon, and his colleagues in the late 1950s [1]. sodium valproate (VPA), later was intubated, and started RE is characterised by inflammation of the cerebral cortex, on midazolam infusion (0.1 mg/kg IV bolus followed by drug-resistant epilepsy, and progressive neurological and 0.125  mg/kg/h infusion) in view of refractory seizures. cognitive deterioration. The 2005 European consensus on Upon shifting to the intensive care unit, he was noted to have pathogenesis, diagnosis, and treatment remains the accepted periodic generalised myoclonus and electroencephalogram guideline for RE [2]. We report an atypical presentation of (EEG) showed generalised slowing with variable interval RE http://www.deepdyve.com/assets/images/DeepDyve-Logo-lg.png Acta Neurologica Belgica Springer Journals

Atypical Rasmussen’s encephalitis presenting as focal status epilepticus and periodic generalised myoclonus

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Publisher
Springer Journals
Copyright
Copyright © The Author(s) under exclusive licence to Belgian Neurological Society 2023
ISSN
0300-9009
eISSN
2240-2993
DOI
10.1007/s13760-023-02267-1
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Abstract

Acta Neurologica Belgica https://doi.org/10.1007/s13760-023-02267-1 LE T TER TO  THE   EDITOR Atypical Rasmussen’s encephalitis presenting as focal status epilepticus and periodic generalised myoclonus 1 2 3 Pavan Kumar Rudrabhatla  · Fazala Mehnaz  · Srinivas Metta Received: 20 September 2022 / Accepted: 5 April 2023 © The Author(s) under exclusive licence to Belgian Neurological Society 2023 Introduction twitching. He was given loading dose of intravenous (IV) phenytoin (PHT) elsewhere, but seizures persisted with no Rasmussen’s encephalitis (RE) is a rare chronic neuro- improvement in sensorium between the events. In the emer- logical disorder, first described by Theodore Rasmussen, gency room he was given loading dose (25 mg/kg) of IV a neurosurgeon, and his colleagues in the late 1950s [1]. sodium valproate (VPA), later was intubated, and started RE is characterised by inflammation of the cerebral cortex, on midazolam infusion (0.1 mg/kg IV bolus followed by drug-resistant epilepsy, and progressive neurological and 0.125  mg/kg/h infusion) in view of refractory seizures. cognitive deterioration. The 2005 European consensus on Upon shifting to the intensive care unit, he was noted to have pathogenesis, diagnosis, and treatment remains the accepted periodic generalised myoclonus and electroencephalogram guideline for RE [2]. We report an atypical presentation of (EEG) showed generalised slowing with variable interval RE

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Acta Neurologica Belgica – Springer Journals

Published: Dec 1, 2023

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